Keywords
polyneuropathy
endocrine diseases
How to Cite
Abstract
POEMS Syndrome is a very rare plasma cell dyscrasia with characteristic symptoms that affect the quality of life of those who suffer it. Diagnostic criteria have been classified as mandatory (two), major (at least one), and minor (at least one) to confirm the suspicion of the disease. The pathophysiology is attributed to the increase in proinflammatory components that cause the symptoms and signs representative of the disease. Currently, therapeutic options available to patients with plasma cell dyscrasia are constantly being studied and advanced, allowing them to be incorporated into these rare conditions and thus offer patients benefits in their quality of life.
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