Keywords
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Abstract
Idiopathic thrombocytopenic purpura (ITP) is an autoimmune disease, with a significant incidence within the population, especially young women. In Paraguay there are no studies on incidence neither on morbidity and mortality. A retrospective, descriptive study of newly diagnosed adult patients with ITP in a referral center was conducted, analyzing demographic, clinical and management characteristics. Of the 80 patients included, there is a predominance of females in young people, although the proportion is equal in older adults. The most frequent reason for consultation was ecchymosis and bruising, and the mean platelet count for diagnosis was 11,000/mm3. Management was similar to that described in the literature with corticosteroids and immunoglobulin when the case required it and it was available. The median time to response was 4 days and mortality was only 4%. This study serves to validate data from large international series, as well as to serve as a guide for centers with similar characteristics.
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