Pure red cell aplasia and primary antiphospholipid syndrome: an autoimmune association
Vol. 25 No. 3 (2021), Clinical case
Vol. 25 No. 3 (2021)

Pure red cell aplasia and primary antiphospholipid syndrome: an autoimmune association: an autoimmune association

Clinical case
Published 2021-12-30
Elie Ghayad
Internal medicine and clinical immunology department, Hôtel-Dieu de France Hospital, Saint-Joseph University, Beirut - Lebanon.
Zeina Kadri
Cardiology department, Hôtel-Dieu de France Hospital, Saint-Joseph University, Beirut - Lebanon.
Fady Haddad
Internal medicine and clinical immunology department, Hôtel-Dieu de France Hospital, Saint-Joseph University, Beirut - Lebanon.
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Keywords

Anemia
Antiphospholipid
Auto-immunity

How to Cite

Ghayad, E., Kadri, Z., & Haddad, F. (2021). Pure red cell aplasia and primary antiphospholipid syndrome: an autoimmune association: an autoimmune association. Journal of Hematology, 25(3), 68–71. Retrieved from https://revistahematologia.com.ar/index.php/Revista/article/view/393
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Abstract

Pure red cell aplasia is an uncommon cause of non-regenerative anemia due to an autoimmune suppression of erythropoiesis. It has been classically associated with systemic lupus erythematosus and rheumatoid arthritis. We report the case of a patient with primary antiphospholipid syndrome who developed severe anemia concordant with pure red cell aplasia. The aforementioned association reinforces the autoimmune basis of pure red cell aplasia.

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