Langerhans cell sarcoma. A case report
Vol. 23 No. 3 (2019), Anatomo-clinic discussion of the hematology fellowships
Vol. 23 No. 3 (2019)

Langerhans cell sarcoma. A case report

Anatomo-clinic discussion of the hematology fellowships
Published 2020-01-13
Maria Belen Castro
Hospital Italiano de Buenos Aires
Maria Agustina Perusini
Hospital Italiano de Buenos Aires
Dana Kohan
Hospital Italiano de Buenos Aires
Dorotea Fantl
Hospital Italiano de Buenos Aires
Victoria Otero
Hospital Italiano de Buenos Aires
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Keywords

Langerhans cell sarcoma
histiocytic neoplasia
Langerhans cells

How to Cite

Castro, M. B., Perusini, M. A., Kohan, D., Fantl, D., & Otero, V. (2020). Langerhans cell sarcoma. A case report. Journal of Hematology, 23(3), 59–62. Retrieved from https://revistahematologia.com.ar/index.php/Revista/article/view/237
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Abstract

Langerhans cell sarcoma is a rare malignant disease with poor prognostic. The diagnosis mainly depends on histopathological evaluation and immunohistochemistry. There is no standardized guide to chemotherapy treatment, which makes it difficult to manage these patients. We present a case of a female patient who presented a torpid evolution despite of the application of multiple treatments, being unable to get benefit from targeted therapies.

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