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© G Arbesú, 2018
Afiliaciones
G Arbesú
Servicio de Hematología. Hospital Humberto Notti. Mendoza
Nuevos tratamientos en hemofilia y enfermedad de von Willebrand
Vol. 22 Núm. Extraordin (2018): Extraordinario II Jornadas Latinoamericanas
Enviado: ene 20, 2019
Publicado: ene 21, 2019
Resumen
La hemofilia es una enfermedad hemorrágica ligada al cromosoma X, producida por la deficiencia del factor VIII (hemofilia A) o IX (hemofilia B)
Las manifestaciones clínicas de la enfermedad sin adecuado tratamiento son los sangrados prolongados, principalmente hemartrosis. Tobillos, rodillas y codos se afectan con mayor frecuencia.
La hemorragia puede ocurrir en cualquier órgano o tejido, particularmente después de un trauma.
El sangrado musculoesquelético es característico en la hemofilia, aunque también puede ocurrir en mucosas, particularmente epistaxis.